English Translation, Synonyms, Definitions and Usage Examples of Spanish Word ‘enfermedad de Degos’. Meanings of “enfermedad de degos” in English Spanish Dictionary: 1 result(s) Meanings of “enfermedad de degos” with other terms in English Spanish. Me llamo Loli tengo 37 años y vivo en Madrid y me diagnoticaron la enfermedad de Degos en despues de que perdiera la vision del ojo.
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Disease definition Malignant atrophic papulosis MAP is a rare, chronic, thrombo-obliterative vasculopathy characterized by papular skin lesions with central porcelain-white atrophy and a surrounding teleangiectatic rim.
enfermedad de Degos – English Translation – Word Magic Spanish-English Dictionary
Therapeutic efforts with anticoagulants and compounds that facilitate blood perfusion, such as acetylosalicylic acid, pentoxifylline, dipyridamole, ticlodipine and heparin have achieved a partial regression of skin lesions in some individual cases.
Differential diagnosis The histology of early lesions resembles cutaneous lupus erythematosus see this term. MAP onset occurs in adults aged with skin lesions that appear initially as small erythematous papules, predominantly on the trunk and the upper extremities. Read this article in English. This condition is chronic and lesions persist over years, often throughout life.
Health care resources for this disease Expert centres 69 Diagnostic tests 0 Patient organisations 21 Orphan drug s 0.
May Pages ee22 Pages For all other comments, regos send your remarks via contact us. All articles are subjected to a rigorous process of revision in pairs, and careful editing for literary and scientific style. Later a wedge-shaped connective tissue necrosis in the deep dermis, due to a thrombotic occlusion of the small arteries and sparse lymphocytes, occurs.
You can change the settings or obtain more information by clicking here. Summary Epidemiology Less than cases have been described in the literature. Specialised Social Services Eurordis directory. In the year has been indexed in the Medlinedatabase, and has become a vehicle for expressing the most current Spanish medicine and modern.
enfermedad de degos
More developed lesions can imitate lichen sclerosus see this term. Si continua navegando, consideramos que acepta su uso.
This item has received. It may more rarely manifest as pericarditis or in other organs encermedad as the lungs, presenting as pleuritis.
Over several days, the center of the lesions sinks and develops a characteristic morphology: Malignant atrophic papulosis MAP is a rare, chronic, thrombo-obliterative vasculopathy characterized by papular skin lesions with central porcelain-white atrophy and a surrounding teleangiectatic rim.
Idiopathic, monosymptomatic, cutaneous presentations are benign, however, systemic manifestations can develop years after the occurrence of skin lesions. The histology of early lesions resembles cutaneous lupus erythematosus see this term. As all patients may potentially develop the systemic, life-threatening variant, an annual follow-up is mandatory.
The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment. The documents contained in this web site are presented for information purposes only.
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Diagnostic methods Diagnosis is based primarily on the cutaneous clinical picture that is nearly pathognomonic. Only comments written in English can be processed. The etiopathogenesis of the disease remains unknown. SNIP measures contextual citation impact by wighting citations based on the total number of citations in a subject field. A clinical inspection of the skin should be combined with additional examinations including brain magnetic resonance tomography, gastroscopy, colonoscopy, X-ray of the chest and abdominal ultrasound, enfermedas order to assess the long-term prognosis.
No effective treatment for the systemic manifestations has been established, however, subcutaneous treprostinil has enfermedsd tested successfully in one case with intestinal and CNS manifestations.
Management and treatment Therapeutic efforts with anticoagulants and compounds that facilitate blood perfusion, such as acetylosalicylic acid, pentoxifylline, dipyridamole, ticlodipine and heparin have achieved a partial regression of skin lesions in some individual cases.
Many patients have been reported to have defects in blood coagulation. Etiology The etiopathogenesis of the disease remains unknown. If you are a member of the AEDV: Previous article Enfermmedad article.
Only comments seeking to improve the quality and accuracy of information on the Orphanet website are accepted. In early stages, histology of lesions may reveal a superficial and deep perivascular lymphocytic infiltration with distinct mucin deposition.
Enfermedad de Degos
Are you a health professional able to prescribe or dispense drugs? Face, scalp, palms of hands and soles of feet are rarely involved.
Pemphigus Vegetans in the Inguinal Folds.